<正>We report the case of a ten-year-old boy who had often presented with respiratory distress since born.Chest X-ray showed an enlarged right ventricle.Echocardiography demonstrated characteristic features of Failot’s tetralogy and the left pulmonary artery could not be visualized.However

cardiac catheterization disclosed that the left pulmonary artery had an anomalous origin in the ascending aorta.The patient underwent total surgical correction of the defects.Nine days later

he was discharged.We present the results of a literature review of the incidence

physiopathological

clinical

diagnostic

and surgical characteristics of this rare disease.